Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV003306794 | SCV004005011 | uncertain significance | Familial thoracic aortic aneurysm and aortic dissection | 2023-04-03 | criteria provided, single submitter | clinical testing | The p.M569V variant (also known as c.1705A>G), located in coding exon 5 of the SKI gene, results from an A to G substitution at nucleotide position 1705. The methionine at codon 569 is replaced by valine, an amino acid with highly similar properties. This amino acid position is conserved. In addition, this alteration is predicted to be deleterious by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |