Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV003444615 | SCV000774462 | likely benign | Epilepsy with myoclonic atonic seizures | 2024-11-03 | criteria provided, single submitter | clinical testing | |
Fulgent Genetics, |
RCV003444615 | SCV000895525 | uncertain significance | Epilepsy with myoclonic atonic seizures | 2018-10-31 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV002388145 | SCV002702855 | uncertain significance | Inborn genetic diseases | 2018-04-12 | criteria provided, single submitter | clinical testing | The p.R479Q variant (also known as c.1436G>A), located in coding exon 12 of the SLC6A1 gene, results from a G to A substitution at nucleotide position 1436. The arginine at codon 479 is replaced by glutamine, an amino acid with highly similar properties. This amino acid position is well conserved in available vertebrate species. In addition, the in silico prediction for this alteration is inconclusive. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |