Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002004906 | SCV002235278 | uncertain significance | not provided | 2021-09-18 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. This sequence change replaces methionine with isoleucine at codon 24 of the SLC34A1 protein (p.Met24Ile). The methionine residue is weakly conserved and there is a small physicochemical difference between methionine and isoleucine. This variant is present in population databases (rs146812061, ExAC 0.009%). This variant has not been reported in the literature in individuals affected with SLC34A1-related conditions. Algorithms developed to predict the effect of missense changes on protein structure and function output the following: SIFT: "Tolerated"; PolyPhen-2: "Benign"; Align-GVGD: "Class C0". The isoleucine amino acid residue is found in multiple mammalian species, which suggests that this missense change does not adversely affect protein function. |
Fulgent Genetics, |
RCV002492105 | SCV002797012 | uncertain significance | Hypophosphatemic nephrolithiasis/osteoporosis 1; Fanconi renotubular syndrome 2; Hypercalcemia, infantile, 2 | 2024-01-09 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV004970645 | SCV005509088 | uncertain significance | Inborn genetic diseases | 2024-10-21 | criteria provided, single submitter | clinical testing | The c.72G>T (p.M24I) alteration is located in exon 2 (coding exon 1) of the SLC34A1 gene. This alteration results from a G to T substitution at nucleotide position 72, causing the methionine (M) at amino acid position 24 to be replaced by an isoleucine (I). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |