Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000518895 | SCV000620278 | uncertain significance | not provided | 2017-08-24 | criteria provided, single submitter | clinical testing | The G74D variant in the SLC22A5 gene has not been reported previously as a pathogenic variant, nor as a benign variant, to our knowledge. The G74D variant is not observed in large population cohorts (Lek et al., 2016; 1000 Genomes Consortium et al., 2015; Exome Variant Server). The G74D variant is a non-conservative amino acid substitution, which occurs at a position that is not conserved. In silico analysis predicts this variant is probably damaging to the protein structure/function. We interpret G74D as a variant of uncertain significance. |
Natera, |
RCV002226467 | SCV002078281 | uncertain significance | Decreased circulating carnitine concentration | 2020-10-14 | no assertion criteria provided | clinical testing | |
Natera, |
RCV001853661 | SCV002107405 | uncertain significance | Renal carnitine transport defect | 2020-10-14 | no assertion criteria provided | clinical testing |