Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Counsyl | RCV000022317 | SCV000791539 | uncertain significance | Renal carnitine transport defect | 2017-05-15 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV000022317 | SCV001413868 | uncertain significance | Renal carnitine transport defect | 2019-10-14 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. This variant has been reported to affect SLC22A5 protein function (PMID: 28841266). This variant has been observed in the homozygous state in an individual affected with primary carnitine deficiency; however, this individual was also found to have a second homozygous variant in the SLC22A5 gene (PMID: 28841266). ClinVar contains an entry for this variant (Variation ID: 25370). This variant is not present in population databases (ExAC no frequency). This sequence change replaces aspartic acid with glycine at codon 115 of the SLC22A5 protein (p.Asp115Gly). The aspartic acid residue is highly conserved and there is a moderate physicochemical difference between aspartic acid and glycine. |
Genome- |
RCV000022317 | SCV002055845 | uncertain significance | Renal carnitine transport defect | 2021-07-15 | criteria provided, single submitter | clinical testing |