Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Eurofins Ntd Llc |
RCV000363931 | SCV000338941 | uncertain significance | not provided | 2016-01-12 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001232748 | SCV001405316 | uncertain significance | Renal carnitine transport defect | 2019-08-06 | criteria provided, single submitter | clinical testing | This sequence change replaces glycine with aspartic acid at codon 12 of the SLC22A5 protein (p.Gly12Asp). The glycine residue is highly conserved and there is a moderate physicochemical difference between glycine and aspartic acid. This variant is not present in population databases (ExAC no frequency). This variant has not been reported in the literature in individuals with SLC22A5-related conditions. ClinVar contains an entry for this variant (Variation ID: 285771). Algorithms developed to predict the effect of missense changes on protein structure and function (SIFT, PolyPhen-2, Align-GVGD) all suggest that this variant is likely to be disruptive, but these predictions have not been confirmed by published functional studies and their clinical significance is uncertain. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Genome- |
RCV001232748 | SCV002055838 | uncertain significance | Renal carnitine transport defect | 2021-07-15 | criteria provided, single submitter | clinical testing |