Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
ARUP Laboratories, |
RCV001001058 | SCV001158179 | uncertain significance | Renal carnitine transport defect | 2019-02-11 | criteria provided, single submitter | clinical testing | The SLC22A5 c.470C>A; p.Ser157Tyr variant, to our knowledge, is not described in the medical literature or in gene-specific databases. It is also absent from general population databases (Exome Variant Server and Genome Aggregation Database), indicating it is not a common polymorphism. The serine at codon 157 is moderately conserved, and computational algorithms (PolyPhen-2, SIFT) predict that this variant is deleterious. However, due to the lack of clinical and functional data regarding this variant, its clinical significance cannot be determined with certainty. |
Natera, |
RCV002226507 | SCV002078304 | uncertain significance | Decreased circulating carnitine concentration | 2021-07-06 | no assertion criteria provided | clinical testing | |
Natera, |
RCV001001058 | SCV002107428 | uncertain significance | Renal carnitine transport defect | 2021-07-06 | no assertion criteria provided | clinical testing |