Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV001755389 | SCV002005570 | likely benign | not provided | 2021-05-06 | criteria provided, single submitter | clinical testing | This variant is associated with the following publications: (PMID: 30936914) |
Labcorp Genetics |
RCV001755389 | SCV002944642 | uncertain significance | not provided | 2023-06-30 | criteria provided, single submitter | clinical testing | ClinVar contains an entry for this variant (Variation ID: 1315727). An algorithm developed to predict the effect of missense changes on protein structure and function (PolyPhen-2) suggests that this variant is likely to be disruptive. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. This missense change has been observed in individual(s) with Waardenburg syndrome (PMID: 30936914). This sequence change replaces serine, which is neutral and polar, with cysteine, which is neutral and slightly polar, at codon 77 of the SNAI2 protein (p.Ser77Cys). This variant is present in population databases (rs372039867, gnomAD 0.2%). |