Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV000623196 | SCV000742314 | uncertain significance | Inborn genetic diseases | 2017-03-16 | criteria provided, single submitter | clinical testing | |
Gene |
RCV001569723 | SCV001793855 | pathogenic | not provided | 2020-07-09 | criteria provided, single submitter | clinical testing | Not observed in large population cohorts (Lek et al., 2016); In silico analysis, which includes protein predictors and evolutionary conservation, supports a deleterious effect; Has not been previously published as pathogenic or benign to our knowledge; This variant is associated with the following publications: (PMID: 15254231, 24886874, 26543203) |
Genetics and Molecular Pathology, |
RCV002466550 | SCV002761486 | uncertain significance | Coffin-Siris syndrome | 2020-11-19 | criteria provided, single submitter | clinical testing | The SOX11 c.356G>C variant is classified as VUS (PS2_Supporting, PM2, PP3) |