Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV003618793 | SCV004514619 | uncertain significance | Hereditary spastic paraplegia 7 | 2023-10-03 | criteria provided, single submitter | clinical testing | This variant, c.466_468dup, results in the insertion of 1 amino acid(s) of the SPG7 protein (p.Asn156dup), but otherwise preserves the integrity of the reading frame. This variant is present in population databases (rs760075114, gnomAD 0.003%). This variant has not been reported in the literature in individuals affected with SPG7-related conditions. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |