Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV003337728 | SCV004047955 | uncertain significance | Hereditary spherocytosis type 3 | criteria provided, single submitter | clinical testing | The missense c.6221C>T (p.Ser2074Phe) variant in SPTA1 gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. The variant is novel (not in any individuals) in gnomAD Exomes and 1000 Genomes. The amino acid Ser at position 2074 is changed to a Phe changing protein sequence and it might alter its composition and physico-chemical properties. The amino acid change p.Ser2074Phe in SPTA1 is predicted as conserved by GERP++ and PhyloP across 100 vertebrates. For these reasons, this variant has been classified as Uncertain Significance. In the absence of second reportable variant the molecular diagnosis is not confirmed. |