Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Foundation for Research in Genetics and Endocrinology, |
RCV004587199 | SCV005077826 | uncertain significance | Iodotyrosyl coupling defect | 2024-07-11 | criteria provided, single submitter | clinical testing | A homozygous missense variant in exon 4 of the TG gene that results in the amino acid substitution of Phenylalanine for Cysteine at codon 92 (p.Cys92Phe; ENST00000220616.9) was detected . The p.Cys92Phe variant has not been reported in the 1000 genomes, gnomAD (v3.1), gnomAD (v2.1) and topmed databases. The in silico predictions of the variant are probably damaging by PolyPhen-2 and damaging by SIFT, LRT, and MutationTaster2. The reference codon is conserved across species. |
Clinical Genetics, |
RCV001730404 | SCV001979298 | uncertain significance | not provided | no assertion criteria provided | clinical testing | ||
Clinical Genetics DNA and cytogenetics Diagnostics Lab, |
RCV001730404 | SCV001980078 | uncertain significance | not provided | no assertion criteria provided | clinical testing |