Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Illumina Laboratory Services, |
RCV000279090 | SCV000472057 | uncertain significance | Iodotyrosyl coupling defect | 2018-01-12 | criteria provided, single submitter | clinical testing | This variant was observed in the ICSL laboratory as part of a predisposition screen in an ostensibly healthy population. It had not been previously curated by ICSL or reported in the Human Gene Mutation Database (HGMD: prior to June 1st, 2018), and was therefore a candidate for classification through an automated scoring system. Utilizing variant allele frequency, disease prevalence and penetrance estimates, and inheritance mode, an automated score was calculated to assess if this variant is too frequent to cause the disease. Based on the score, this variant could not be ruled out of causing disease and therefore its association with disease required further investigation. A literature search was performed for the gene, cDNA change, and amino acid change (if applicable). No publications were found based on this search. This variant was therefore classified as a variant of unknown significance for this disease. |
Fulgent Genetics, |
RCV002480249 | SCV002792720 | uncertain significance | Iodotyrosyl coupling defect; Autoimmune thyroid disease, susceptibility to, 3 | 2021-10-07 | criteria provided, single submitter | clinical testing | |
Prevention |
RCV004555562 | SCV004113472 | uncertain significance | TG-related disorder | 2022-10-14 | criteria provided, single submitter | clinical testing | The TG c.4982G>A variant is predicted to result in the amino acid substitution p.Arg1661His. This variant was reported in an individual with congenital hypothyroidism together with a nonsense variant in DUOX2 gene (Table S1, Wang et al. 2020. PubMed ID: 32425884). This variant is reported in 0.11% of alleles in individuals of East Asian descent in gnomAD (http://gnomad.broadinstitute.org/variant/8-133948050-G-A). At this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |