Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000579262 | SCV000681070 | pathogenic | not provided | 2017-11-17 | criteria provided, single submitter | clinical testing | The K36X pathogenic variant in the TGFB3 gene has not been reported as a pathogenic or benign to our knowledge. This variant is predicted to cause loss of normal protein function either by protein truncation or nonsense-mediated mRNA decay. Other loss of function variants in the TGFB3 gene have been reported in Human Gene Mutation Database in association with TGFB3-related disorders (Stenson et al., 2014). Furthermore, the K36X variant is not observed in large population cohorts (Lek et al., 2016). |