Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV002448016 | SCV002676394 | uncertain significance | Familial thoracic aortic aneurysm and aortic dissection | 2022-01-17 | criteria provided, single submitter | clinical testing | The p.R287Q variant (also known as c.860G>A), located in coding exon 5 of the TGFB3 gene, results from a G to A substitution at nucleotide position 860. The arginine at codon 287 is replaced by glutamine, an amino acid with highly similar properties. This amino acid position is conserved. In addition, the in silico prediction for this alteration is inconclusive. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Dept of Medical Biology, |
RCV003318419 | SCV004021952 | uncertain significance | Long QT syndrome | 2024-01-08 | criteria provided, single submitter | research | Criteria: PM2 |