Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute of Medical Genetics and Applied Genomics, |
RCV004017188 | SCV004847106 | likely pathogenic | Loeys-Dietz syndrome 2 | 2024-04-18 | criteria provided, single submitter | clinical testing | Detected in a single individual (heterozygous). The deletion abrogates the genuine splice donor but it creates a potent novel one. The most likely effect on the level of protein is therefore a deletion of 5 amino acids (p.Ala414_Gln418del). |