Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ce |
RCV001093079 | SCV001249892 | pathogenic | not provided | 2019-11-01 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001093079 | SCV003439373 | pathogenic | not provided | 2024-07-16 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Ser210*) in the TULP1 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in TULP1 are known to be pathogenic (PMID: 8606774, 10549638, 15024725, 18055821). This variant is not present in population databases (gnomAD no frequency). This premature translational stop signal has been observed in individual(s) with retinitis pigmentosa (PMID: 23591405). ClinVar contains an entry for this variant (Variation ID: 872549). For these reasons, this variant has been classified as Pathogenic. |
Fulgent Genetics, |
RCV005036403 | SCV005671272 | pathogenic | Retinitis pigmentosa 14; Leber congenital amaurosis 15 | 2024-04-17 | criteria provided, single submitter | clinical testing |