Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Prevention |
RCV004528699 | SCV004108373 | uncertain significance | UMOD-related disorder | 2023-05-25 | criteria provided, single submitter | clinical testing | The UMOD c.200A>G variant is predicted to result in the amino acid substitution p.Asp67Gly. This variant was reported in an individual with end-stage kidney disease (Kidd et al. 2020. PubMed ID: 32954071, supplementary table 1). This variant has not been reported in a large population database (http://gnomad.broadinstitute.org), indicating this variant is rare. At this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |
Fulgent Genetics, |
RCV005012927 | SCV005638555 | uncertain significance | Familial juvenile hyperuricemic nephropathy type 1 | 2024-06-03 | criteria provided, single submitter | clinical testing |