Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV002854209 | SCV003619035 | uncertain significance | Inborn genetic diseases | 2022-05-18 | criteria provided, single submitter | clinical testing | The c.311G>T (p.S104I) alteration is located in exon 3 (coding exon 3) of the VLDLR gene. This alteration results from a G to T substitution at nucleotide position 311, causing the serine (S) at amino acid position 104 to be replaced by an isoleucine (I). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Revvity Omics, |
RCV003485827 | SCV004237521 | uncertain significance | Cerebellar ataxia, intellectual disability, and dysequilibrium syndrome 1 | 2023-10-31 | criteria provided, single submitter | clinical testing |