Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Diagnostics Services |
RCV003445297 | SCV004171815 | pathogenic | Gabriele de Vries syndrome | 2023-12-19 | criteria provided, single submitter | clinical testing | The c.1025G>A variant is not present in publicly available population databases like 1000 Genomes, EVS, gnomAD, ExAC, Indian Exome Database or our in-house exome database. This variant has neither been published in literature nor reported to clinical databases like Human Genome Mutation Database (HGMD), OMIM or ClinVar in any affected individuals. In-silico pathogenicity prediction programs like PolyPhen-2, MutationTaster2, CADD etc predicted this variant to be likely deleterious, however these predictions were not confirmed by published functional studies. This variant is not present in the parents of our patients. |
Juno Genomics, |
RCV003445297 | SCV005418524 | uncertain significance | Gabriele de Vries syndrome | criteria provided, single submitter | clinical testing | PM2_Supporting+PM6_Supporting+PP4+PP2 |