Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Center for Genomics, |
RCV000768255 | SCV000898792 | uncertain significance | Kabuki syndrome 1 | 2018-05-25 | criteria provided, single submitter | clinical testing | KMT2D NM_003482.3 exon 10 p.Pro470Ser (c.1408C>T): This variant has not been reported in the literature but is present in 1/33394 Latino alleles in the Genome Aggregation Database (http://gnomad.broadinstitute.org/rs761594079). Evolutionary conservation and computational predictive tools for this variant are unclear. In summary, data on this variant is insufficient for disease classification. Therefore, the clinical significance of this variant is uncertain. |
Labcorp Genetics |
RCV002533939 | SCV003250095 | benign | Kabuki syndrome | 2024-10-25 | criteria provided, single submitter | clinical testing | |
Center for Genomics, |
RCV003224446 | SCV003920127 | uncertain significance | Kabuki syndrome 1; Choanal atresia-athelia-hypothyroidism-delayed puberty-short stature syndrome | 2021-03-30 | criteria provided, single submitter | clinical testing | KMT2D NM_003482.3 exon 10 p.Pro470Ser (c.1408C>T): This variant has not been reported in the literature but is present in 1/33394 Latino alleles in the Genome Aggregation Database (http://gnomad.broadinstitute.org/rs761594079). Evolutionary conservation and computational predictive tools for this variant are unclear. In summary, data on this variant is insufficient for disease classification. Therefore, the clinical significance of this variant is uncertain. |