Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genetic Services Laboratory, |
RCV000146223 | SCV000193463 | uncertain significance | Kabuki syndrome 1 | 2014-01-08 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001857514 | SCV002208958 | benign | Kabuki syndrome | 2023-11-07 | criteria provided, single submitter | clinical testing | |
New York Genome Center | RCV000146223 | SCV002564308 | uncertain significance | Kabuki syndrome 1 | 2021-09-03 | criteria provided, single submitter | clinical testing | |
Prevention |
RCV004758649 | SCV005363324 | uncertain significance | KMT2D-related disorder | 2024-08-30 | no assertion criteria provided | clinical testing | The KMT2D c.6640G>A variant is predicted to result in the amino acid substitution p.Ala2214Thr. This variant was reported in an individual with Kabuki syndrome in a meta-analysis of KMT2D missense variants (Supplemental Table S3-1, Faundes et al. 2019. PubMed ID: 30459467). This variant is reported in 0.0024% of alleles in individuals of European (Non-Finnish) descent in gnomAD. At this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |