Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002518542 | SCV003444338 | uncertain significance | not provided | 2022-05-31 | criteria provided, single submitter | clinical testing | This sequence change affects codon 106 of the CDC45 mRNA. It is a 'silent' change, meaning that it does not change the encoded amino acid sequence of the CDC45 protein. RNA analysis indicates that this variant induces altered splicing and likely results in a shortened protein product. This variant is present in population databases (rs745800041, gnomAD 0.01%). This variant has been observed in individual(s) with clinical features of CDC45-related conditions (PMID: 27374770). ClinVar contains an entry for this variant (Variation ID: 253098). Studies have shown that this variant results in skipping of exon 4, but is expected to preserve the integrity of the reading-frame (PMID: 27374770). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
OMIM | RCV000239576 | SCV000297896 | pathogenic | Meier-Gorlin syndrome 7 | 2016-10-20 | no assertion criteria provided | literature only |