Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
3billion | RCV002284165 | SCV003841664 | likely pathogenic | Ciliary dyskinesia, primary, 48, without situs inversus | 2023-02-23 | criteria provided, single submitter | clinical testing | The variant is observed at an extremely low frequency in the gnomAD v2.1.1 dataset (total allele frequency: 0.001%). This variant was predicted to result in a loss or disruption of normal protein function through protein truncation. The predicted truncated protein may be shortened by more than 10%. Therefore, this variant is classified as Likely pathogenic according to the recommendation of ACMG/AMP guideline. |
OMIM | RCV002284165 | SCV002573545 | pathogenic | Ciliary dyskinesia, primary, 48, without situs inversus | 2022-09-15 | no assertion criteria provided | literature only |