Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genetic Services Laboratory, |
RCV001819319 | SCV002069474 | uncertain significance | not specified | 2018-08-28 | criteria provided, single submitter | clinical testing | |
Fulgent Genetics, |
RCV002482360 | SCV002775463 | uncertain significance | Maturity-onset diabetes of the young type 7 | 2021-08-19 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV003718438 | SCV004508645 | uncertain significance | not provided | 2023-09-30 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. An algorithm developed to predict the effect of missense changes on protein structure and function (PolyPhen-2) suggests that this variant is likely to be disruptive. ClinVar contains an entry for this variant (Variation ID: 1336833). This missense change has been observed in individual(s) with dyslipidemia (PMID: 32041611). This variant is present in population databases (rs757875185, gnomAD 0.002%). This sequence change replaces serine, which is neutral and polar, with cysteine, which is neutral and slightly polar, at codon 466 of the KLF11 protein (p.Ser466Cys). |