Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV004097101 | SCV003554279 | uncertain significance | Primary ciliary dyskinesia | 2021-03-02 | criteria provided, single submitter | clinical testing | The c.2966A>T (p.D989V) alteration is located in exon 22 (coding exon 22) of the OFD1 gene. This alteration results from a A to T substitution at nucleotide position 2966, causing the aspartic acid (D) at amino acid position 989 to be replaced by a valine (V). The in silico prediction for the p.D989V alteration is inconclusive. Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Revvity Omics, |
RCV003134697 | SCV003814255 | uncertain significance | not provided | 2019-10-30 | criteria provided, single submitter | clinical testing |