Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
MGZ Medical Genetics Center | RCV002290381 | SCV002580506 | likely pathogenic | Intellectual developmental disorder with gastrointestinal difficulties and high pain threshold | 2021-10-27 | criteria provided, single submitter | clinical testing | |
Gene |
RCV004719251 | SCV005325118 | likely pathogenic | not provided | 2023-07-17 | criteria provided, single submitter | clinical testing | Identified as mosaic in individuals with either breast or ovarian cancer following chemotherapy (Pharoah et al., 2016; Ruark et al., 2013); Nonsense variant predicted to result in protein truncation, as the last 144 amino acids are lost, and other loss-of-function variants have been reported downstream in HGMD; Not observed at significant frequency in large population cohorts (gnomAD); This variant is associated with the following publications: (PMID: 26823519, 23242139) |