Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Baylor Genetics | RCV000679953 | SCV000807387 | pathogenic | Arthrogryposis, distal, type 1A | 2017-09-01 | criteria provided, single submitter | clinical testing | This nonsense mutation is categorized as deleterious according to ACMG guidelines (PMID:18414213). It was found once in our laboratory in a homozygous state in a newborn male with correctable distal arthrogryposis, areflexia, mild micrognathia, deceased from respiratory failure/severe hypotonia. There were previously affected sibs (not tested), and this family has been reported in abstract form (DOI:10.1007/s10897-014-9778-4) |
Section for Clinical Neurogenetics, |
RCV001030776 | SCV001156083 | pathogenic | Neuropathy, congenital hypomyelinating, 3 | 2019-08-01 | no assertion criteria provided | research |