Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genomics, |
RCV004577697 | SCV005061569 | likely pathogenic | Hermansky-Pudlak syndrome 2 | 2024-06-14 | criteria provided, single submitter | clinical testing | equency: The variant is absent from the gnomAD reference population dataset. Phenotype: The patient's phenotype or family history is highly specific for a disease with a single genetic etiology Prediction tools: REVEL predicts a deleterious effect on the gene or gene product (score 0.88). Clinical evidence: To date, the variant has not been described by reputable sources or in the primary literature. (pm2_support, pp3_modarate, pm3_support, pp4_strong) |