Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000559680 | SCV000659687 | pathogenic | TP63-Related Spectrum Disorders | 2019-03-13 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. Algorithms developed to predict the effect of missense changes on protein structure and function are either unavailable or do not agree on the potential impact of this missense change (SIFT: "Deleterious"; PolyPhen-2: "Probably Damaging"; Align-GVGD: "Class C0"). This variant has been reported in several individuals affected with ectodermal dysplasia, and has been observed to be de novo in at least one individual (PMID: 16691622, Invitae). ClinVar contains an entry for this variant (Variation ID: 478110). This variant is not present in population databases (ExAC no frequency). This sequence change replaces histidine with tyrosine at codon 247 of the TP63 protein (p.His247Tyr). The histidine residue is highly conserved and there is a moderate physicochemical difference between histidine and tyrosine. |
Hudson |
RCV000851194 | SCV000993444 | likely pathogenic | Ectrodactyly, ectodermal dysplasia, and cleft lip-palate syndrome 3 | 2019-08-26 | criteria provided, single submitter | research | ACMG codes: PS4M, PM2, PP3, PP5 |