Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ce |
RCV001311426 | SCV001501592 | pathogenic | not provided | 2021-07-01 | criteria provided, single submitter | clinical testing | |
Immunogenetics of Pediatric Autoimmune Diseases, |
RCV001254899 | SCV001430915 | likely pathogenic | Autoimmune hemolytic anemia; Autoimmune thrombocytopenia | 2020-01-01 | no assertion criteria provided | research | |
Department of Immunology, |
RCV004719119 | SCV005326493 | pathogenic | Autoinflammatory syndrome with immunodeficiency | 2022-01-08 | no assertion criteria provided | clinical testing | The SOCS1 c.480_481insGCCGC (p.M161Afs*46) variant is classified as pathogenic based on it being a frameshift insertion predicted to result in a truncated or absent protein (PVS1), its rarity in population databases (PM2_Supporting), and published literature and ClinVar entries supporting its role in autoimmune disease (PS4). This variant is associated with autosomal dominant Autoimmune inflammatory syndrome, familial, with or without immunodeficiency (OMIM: 619375), which is characterized by a variety of autoimmune features. |