Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001890512 | SCV002155323 | likely benign | Neuronal ceroid lipofuscinosis 13 | 2024-10-24 | criteria provided, single submitter | clinical testing | |
Center for Genomics, |
RCV001890512 | SCV003919863 | uncertain significance | Neuronal ceroid lipofuscinosis 13 | 2022-07-22 | criteria provided, single submitter | clinical testing | This variant has not been reported in the literature but is present in the Genome Aggregation Database (Highest reported MAF 0.01% (3/15270) (https://gnomad.broadinstitute.org/variant/11-66568327-G-T?dataset=gnomad_r3). This variant is present in ClinVar (Variation ID:1382735). Evolutionary conservation and computational predictive tools for this variant are limited or unavailable. Of note, this variant is a silent variant and does not change the amino acid, reducing the probability that this variant is disease causing. In summary, data on this variant is insufficient for disease classification. Therefore, the clinical significance of this variant is uncertain. |
Gene |
RCV005235602 | SCV005882188 | uncertain significance | not provided | 2024-09-09 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis indicates that this variant does not alter splicing; Has not been previously published as pathogenic or benign to our knowledge |