Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratory for Molecular Medicine, |
RCV000215328 | SCV000269353 | benign | not specified | 2015-06-10 | criteria provided, single submitter | clinical testing | c.2384+4A>T in intron 16 of MYOM1: This variant is not expected to have clinical significance because it has been identified in 1.0% (98/9464) of African chromo somes by the Exome Aggregation Consortium (ExAC, http://exac.broadinstitute.org; dbSNP rs73373171). |
Invitae | RCV000462020 | SCV000561221 | benign | Hypertrophic cardiomyopathy | 2024-01-31 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV000621548 | SCV000739897 | likely benign | Cardiovascular phenotype | 2013-04-25 | criteria provided, single submitter | clinical testing | Does not segregate with disease in family study (genes with incomplete penetrance);Subpopulation frequency in support of benign classification |
Prevention |
RCV004530276 | SCV004735889 | benign | MYOM1-related disorder | 2019-05-06 | criteria provided, single submitter | clinical testing | This variant is classified as benign based on ACMG/AMP sequence variant interpretation guidelines (Richards et al. 2015 PMID: 25741868, with internal and published modifications). |
Stanford Center for Inherited Cardiovascular Disease, |
RCV000215328 | SCV000280392 | uncertain significance | not specified | 2013-01-07 | no assertion criteria provided | clinical testing | Note this variant was found in clinical genetic testing performed by one or more labs who may also submit to ClinVar. Thus any internal case data may overlap with the internal case data of other labs. The interpretation reviewed below is that of the Stanford Center for Inherited Cardiovascular Disease. Splice site variant (c.2384+4 A>T) in the MYOM1 gene Based on the information reviewed below, we categorize it as a VUS, probably benign due to its frequency in African Americans in population datasets. (Our patient is African American.) The c.2384+4 A>T variant is located in intron 16 of the MYOM1 gene, four nucleotides after exon 16. This variant was previously reported in the SNPDatabase as rs73373171. Based on data from the NHLBI Exome Sequencing Project (ESP), the T-allele has an overall frequency of approximately 0.23% (23/9,826), having been observed in 0.73% (23/3,154) of African American alleles, and in 0.0% (0/6,672) of European American alleles. Based on data from the 1000 Genomes Project, the A-allele has an overall frequency of approximately 0.23% (5/2,188). The highest observed frequency was 3 of 194 (1.55%) Luhya West African chromosomes studied. Based on nucleotide sequence alignment in 37 available vertebrate species, this nucleotide position is conserved in 35 of them. Using the BDGP and ESEfinder splice site prediction tools, this alteration is predicted to abolish the native donor splice site; however, direct evidence of the effect on splicing is unavailable. |