Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratory for Molecular Medicine, |
RCV000218386 | SCV000269365 | benign | not specified | 2014-11-24 | criteria provided, single submitter | clinical testing | Thr154Met in exon 4 of MYOM1: This variant is not expected to have clinical sign ificance because it has been identified in 5.2% (10/194) of Luhya (Kenyan) chrom osomes from a broad population by the 1000 Genomes Project (http://www.ncbi.nlm. nih.gov/projects/SNP; dbSNP rs140845661). |
Labcorp Genetics |
RCV000474356 | SCV000561254 | benign | Hypertrophic cardiomyopathy | 2024-01-25 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV000218386 | SCV002639142 | uncertain significance | not specified | 2022-09-08 | criteria provided, single submitter | clinical testing | The p.T154M variant (also known as c.461C>T), located in coding exon 3 of the MYOM1 gene, results from a C to T substitution at nucleotide position 461. The threonine at codon 154 is replaced by methionine, an amino acid with similar properties. This amino acid position is conserved. In addition, this alteration is predicted to be tolerated by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Center for Genomics, |
RCV003227717 | SCV003924132 | uncertain significance | not provided | 2021-03-30 | criteria provided, single submitter | clinical testing | MYOM1 NM_003803.3 exon 4 p.Thr145Met (c.461C>T): This variant has not been reported in the literature and is present in 0.6% (152/23992) of African alleles in the Genome Aggregation Database (http://gnomad.broadinstitute.org/variant/18-3189056-G-A). This variant is present in ClinVar (Variation ID:226824). Evolutionary conservation and computational predictive tools suggest that this variant may impact the protein. In summary, data on this variant is insufficient for disease classification. Therefore, the clinical significance of this variant is uncertain. |
Prevention |
RCV004541311 | SCV004760660 | benign | MYOM1-related disorder | 2019-11-20 | no assertion criteria provided | clinical testing | This variant is classified as benign based on ACMG/AMP sequence variant interpretation guidelines (Richards et al. 2015 PMID: 25741868, with internal and published modifications). |