Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Foundation for Research in Genetics and Endocrinology, |
RCV002291519 | SCV002583560 | uncertain significance | Mitochondrial DNA depletion syndrome 9 | 2021-09-28 | criteria provided, single submitter | clinical testing | A homozygous missense variation in exon 4 of the SUCLG1 gene that results in the amino acid substitution of Serine for Asparagine at codon 171 was detected. The observed variant c.512A>G (p.Asn171Ser) has not been reported in the 1000 genomes and has minor allele frequency of 0.0006% in the gnomAD database. The in silico prediction of the variant are possibly damaging by PolyPhen-2 (HumDiv) and damaging by MutationTaster2, LRT and SIFT. The reference codon is conserved across species. In summary, the variant meets our criteria to be classified as a variant of uncertain significance. |