Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute of Medical Genetics and Applied Genomics, |
RCV002464962 | SCV002759324 | likely pathogenic | Mitochondrial DNA depletion syndrome 9 | 2022-12-07 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV002464962 | SCV003003194 | uncertain significance | Mitochondrial DNA depletion syndrome 9 | 2022-03-19 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function (SIFT, PolyPhen-2, Align-GVGD) all suggest that this variant is likely to be disruptive. This variant has not been reported in the literature in individuals affected with SUCLG1-related conditions. This variant is not present in population databases (gnomAD no frequency). This sequence change replaces leucine, which is neutral and non-polar, with arginine, which is basic and polar, at codon 240 of the SUCLG1 protein (p.Leu240Arg). |