Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV003380106 | SCV004096207 | uncertain significance | Hereditary cancer-predisposing syndrome | 2023-07-20 | criteria provided, single submitter | clinical testing | The p.T205S variant (also known as c.614C>G), located in coding exon 3 of the PHOX2B gene, results from a C to G substitution at nucleotide position 614. The threonine at codon 205 is replaced by serine, an amino acid with similar properties. This amino acid position is conserved. In addition, this alteration is predicted to be tolerated by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Baylor Genetics | RCV003475571 | SCV004203988 | uncertain significance | Neuroblastoma, susceptibility to, 2 | 2023-06-25 | criteria provided, single submitter | clinical testing |