Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV001026851 | SCV001189316 | uncertain significance | Hereditary cancer-predisposing syndrome | 2023-10-11 | criteria provided, single submitter | clinical testing | The p.Y261C variant (also known as c.782A>G), located in coding exon 5 of the AIP gene, results from an A to G substitution at nucleotide position 782. The tyrosine at codon 261 is replaced by cysteine, an amino acid with highly dissimilar properties. This amino acid position is highly conserved in available vertebrate species. In addition, this alteration is predicted to be deleterious by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Labcorp Genetics |
RCV001039474 | SCV001203006 | uncertain significance | not provided | 2023-12-06 | criteria provided, single submitter | clinical testing | This sequence change replaces tyrosine, which is neutral and polar, with cysteine, which is neutral and slightly polar, at codon 261 of the AIP protein (p.Tyr261Cys). This variant is present in population databases (rs780149133, gnomAD 0.003%). This variant has not been reported in the literature in individuals affected with AIP-related conditions. ClinVar contains an entry for this variant (Variation ID: 827274). Advanced modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) performed at Invitae indicates that this missense variant is expected to disrupt AIP protein function with a positive predictive value of 80%. RNA analysis performed to evaluate the impact of this missense change on mRNA splicing indicates it does not significantly alter splicing (Invitae). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Baylor Genetics | RCV004570076 | SCV005059590 | uncertain significance | Somatotroph adenoma | 2023-12-28 | criteria provided, single submitter | clinical testing |