Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute of Human Genetics, |
RCV002246164 | SCV002515877 | likely pathogenic | Epilepsy, familial focal, with variable foci 2 | 2022-05-20 | criteria provided, single submitter | clinical testing | For the following reasons, we consider the detected NPR2 mutation as likely pathogenic: the mutation has already been described as likely pathogenic in affected individuals (HGMD: CM187911; et al. Hauer NN et al. (2018) Genet Med. 20(6): 630-638); the mutation is located in a protein domain of NPR2 and affects a moderately conserved amino acid; a comparison with the gnomAD browser did not provide evidence that this sequence change is a norm variant that can also be detected in non-affected individuals; the mutation is independently classified as deleterious by the majority (n=15 of 20) of the prediction programs; both affected brothers are carriers of the above mutation; the following ACMG criteria were used for classification: PM1, PM2, PP1, PP2, PP3. |