Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Medical Genetics, |
RCV000234850 | SCV000280581 | pathogenic | Palmoplantar keratoderma-deafness syndrome | 2016-04-26 | no assertion criteria provided | clinical testing | Variant predicted to result in aminoacid change not previously reported in patients with disease. Variant detected in four affected family members. |