Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000413562 | SCV000491189 | pathogenic | not provided | 2017-08-18 | criteria provided, single submitter | clinical testing | The c.1602+1 G>A variant has been reported previously in association with Becker muscular dystrophy (Deburgrave et al., 2007). This variant destroys the canonical splice donor site for intron 13. RNA analysis confirmed c.1602+1 G>A produces a full length DMD transcript, as well as a second in-frame transcript with exon 13 skipped, and results in decreased dystrophin (Deburgrave et al., 2007). This variant was not observed in approximately 6,500 individuals of European and African American ancestry in the NHLBI Exome Sequencing Project, indicating it is not a common benign variant in these populations. |