Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Eurofins Ntd Llc |
RCV000730416 | SCV000858150 | pathogenic | not provided | 2017-12-01 | criteria provided, single submitter | clinical testing | |
Revvity Omics, |
RCV000730416 | SCV002019340 | pathogenic | not provided | 2020-01-28 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001868955 | SCV002234649 | pathogenic | Duchenne muscular dystrophy | 2021-06-12 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. This variant has been reported in individuals in the Leiden Open-source Variation Database (PMID: 21520333). ClinVar contains an entry for this variant (Variation ID: 594994). This variant is not present in population databases (ExAC no frequency). This sequence change creates a premature translational stop signal (p.Tyr972Metfs*32) in the DMD gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in DMD are known to be pathogenic (PMID: 16770791, 25007885). |