Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Myriad Genetics, |
RCV001263947 | SCV001442045 | likely pathogenic | Becker muscular dystrophy; Duchenne muscular dystrophy | 2019-03-01 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV002537663 | SCV003496218 | pathogenic | Duchenne muscular dystrophy | 2022-10-10 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. Algorithms developed to predict the effect of sequence changes on RNA splicing suggest that this variant may create or strengthen a splice site. ClinVar contains an entry for this variant (Variation ID: 983942). This premature translational stop signal has been observed in individual(s) with Becker muscular dystrophy (PMID: 33420945). This variant is not present in population databases (gnomAD no frequency). This sequence change creates a premature translational stop signal (p.Trp1660*) in the DMD gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in DMD are known to be pathogenic (PMID: 16770791, 25007885). |