Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV003338204 | SCV004047214 | likely pathogenic | Duchenne muscular dystrophy | criteria provided, single submitter | clinical testing | The frame shift variant c.5574_5575del (p.His1858GlnfsTer29) in DMD gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. The p.His1858GlnfsTer29 variant is novel (not in any individuals) in gnomAD Exomes and 1000 Genomes. This variant causes a frameshift starting with codon Histidine 1858, changes this amino acid to Glutamine residue, and creates a premature Stop codon at position 29 of the new reading frame, denoted p.His1858GlnfsTer29. For these reasons, this variant has been classified as Likely Pathogenic |