Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV000012042 | SCV005438846 | pathogenic | Duchenne muscular dystrophy | 2023-07-22 | criteria provided, single submitter | clinical testing | The observed stop gained c.5985T>Gp.Tyr1995Ter variant in DMD gene has been reported previously in X-linked state in individuals affected with Duchenne muscular dystrophy Tran et al., 2007. This variant is absent in gnomAD Exomes. This variant has been reported to the ClinVar database as Pathogenic. This variant is predicted to cause loss of normal protein function either through protein truncation or nonsense-mediated mRNA decay. Loss of function variants have been previously reported to be disease causing. Computational evidence MutationTaster - Disease causing automatic predicts damaging effect on protein structure and function for this variant. For these reasons, this variant has been classified as Pathogenic. |
OMIM | RCV000012042 | SCV000032276 | pathogenic | Duchenne muscular dystrophy | 2007-01-01 | no assertion criteria provided | literature only |