Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000473580 | SCV000550297 | pathogenic | Duchenne muscular dystrophy | 2019-07-04 | criteria provided, single submitter | clinical testing | This variant has been observed in several individuals affected with Duchenne muscular dystrophy (PMID: 11524473, 19937601 ). ClinVar contains an entry for this variant (Variation ID: 409914). For these reasons, this variant has been classified as Pathogenic. Donor and acceptor splice site variants typically lead to a loss of protein function (PMID: 16199547), and loss-of-function variants in DMD are known to be pathogenic (PMID: 16770791, 25007885). This variant is not present in population databases (ExAC no frequency). This sequence change affects a donor splice site in intron 45 of the DMD gene. It is expected to disrupt RNA splicing and likely results in an absent or disrupted protein product. |
ARUP Laboratories, |
RCV000507494 | SCV000603353 | pathogenic | not specified | 2016-12-07 | criteria provided, single submitter | clinical testing |