Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genetic Services Laboratory, |
RCV000192688 | SCV000247192 | likely pathogenic | Duchenne muscular dystrophy | 2014-10-08 | criteria provided, single submitter | clinical testing | |
Eurofins Ntd Llc |
RCV000727646 | SCV000854938 | likely pathogenic | not provided | 2017-10-04 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV000192688 | SCV002248837 | likely pathogenic | Duchenne muscular dystrophy | 2021-08-12 | criteria provided, single submitter | clinical testing | ClinVar contains an entry for this variant (Variation ID: 210853). This variant has been observed in individual(s) with Duchenne muscular dystrophy (PMID: 18059005). The frequency data for this variant in the population databases is considered unreliable, as metrics indicate insufficient coverage at this position in the ExAC database. This sequence change falls in intron 45 of the DMD gene. It does not directly change the encoded amino acid sequence of the DMD protein. RNA analysis indicates that this variant induces altered splicing and may result in an absent or disrupted protein product. In summary, the currently available evidence indicates that the variant is pathogenic, but additional data are needed to prove that conclusively. Therefore, this variant has been classified as Likely Pathogenic. Studies have shown that this variant results in altered splicing, which introduces a premature termination codon (PMID: 18059005). The resulting mRNA is expected to undergo nonsense-mediated decay. |
Women's Health and Genetics/Laboratory Corporation of America, |
RCV004700578 | SCV005204262 | likely pathogenic | Qualitative or quantitative defects of dystrophin | 2024-06-13 | criteria provided, single submitter | clinical testing | Variant summary: DMD c.6614+3310G>T is located at a position not widely known to affect splicing. Several computational tools predict a significant impact on normal splicing: Three predict the variant creates a cryptic 5' donor site. At least one publication reports experimental evidence that this variant affects mRNA splicing (Gurvich_2008). The frequency of this variant in the general population could not be determined as the technology used for large population databases (ExAC, gnomAD, ESP, 1000G) cannot detect variants of this type. c.6614+3310G>T has been reported in the literature in individuals affected with Muscular dystrophy, Duchenne (DMD) (example: Gurvich_2008). The following publication has been ascertained in the context of this evaluation (PMID: 18059005). ClinVar contains an entry for this variant (Variation ID: 210853). Based on the evidence outlined above, the variant was classified as likely pathogenic. |
Fulgent Genetics, |
RCV005042411 | SCV005682865 | likely pathogenic | Becker muscular dystrophy; Duchenne muscular dystrophy; Dilated cardiomyopathy 3B | 2024-06-14 | criteria provided, single submitter | clinical testing |