Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV000248044 | SCV000319992 | uncertain significance | Cardiovascular phenotype | 2024-09-13 | criteria provided, single submitter | clinical testing | The p.R2477W variant (also known as c.7429C>T), located in coding exon 51 of the DMD gene, results from a C to T substitution at nucleotide position 7429. The arginine at codon 2477 is replaced by tryptophan, an amino acid with dissimilar properties. Based on data from gnomAD, the T allele has an overall frequency of 0.0044% (8/183223) total alleles studied, with 2 hemizygote(s) observed. The highest observed frequency was 0.0361% (5/13856) of East Asian alleles. This amino acid position is not well conserved in available vertebrate species. In addition, this alteration is predicted to be tolerated by in silico analysis. Based on the available evidence, the clinical significance of this variant remains unclear. |
Labcorp Genetics |
RCV001067594 | SCV001232662 | likely benign | Duchenne muscular dystrophy | 2024-11-09 | criteria provided, single submitter | clinical testing | |
Fulgent Genetics, |
RCV002479986 | SCV002788622 | uncertain significance | Becker muscular dystrophy; Duchenne muscular dystrophy; Dilated cardiomyopathy 3B | 2021-07-17 | criteria provided, single submitter | clinical testing | |
Natera, |
RCV001828166 | SCV002087768 | uncertain significance | Becker muscular dystrophy; Duchenne muscular dystrophy; Cardiomyopathy; Dystrophin deficiency | 2020-06-25 | no assertion criteria provided | clinical testing |