Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001978413 | SCV002269580 | uncertain significance | Amyotrophic lateral sclerosis type 1; Perry syndrome; Neuronopathy, distal hereditary motor, type 7B | 2022-07-13 | criteria provided, single submitter | clinical testing | Algorithms developed to predict the effect of missense changes on protein structure and function (SIFT, PolyPhen-2, Align-GVGD) all suggest that this variant is likely to be disruptive. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. ClinVar contains an entry for this variant (Variation ID: 1489826). This variant has not been reported in the literature in individuals affected with DCTN1-related conditions. This variant is present in population databases (rs370192633, gnomAD 0.003%). This sequence change replaces glycine, which is neutral and non-polar, with alanine, which is neutral and non-polar, at codon 601 of the DCTN1 protein (p.Gly601Ala). |
Ai |
RCV002224133 | SCV002502180 | uncertain significance | not provided | 2022-03-05 | criteria provided, single submitter | clinical testing | |
Prevention |
RCV003408053 | SCV004111777 | uncertain significance | DCTN1-related disorder | 2022-10-18 | criteria provided, single submitter | clinical testing | The DCTN1 c.1802G>C variant is predicted to result in the amino acid substitution p.Gly601Ala. This variant was reported in a study of individuals with familial amyotrophic lateral sclerosis (FALS), although no additional evidence was provided that could help establish its pathogenicity (reported as G601A in Corcia et al. 2021. PubMed ID: 33408239). This variant is reported in 0.0026% of alleles in individuals of European (Non-Finnish) descent in gnomAD (http://gnomad.broadinstitute.org/variant/2-74595907-C-G). At this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |