Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV001593455 | SCV001816460 | likely benign | not provided | 2019-12-05 | criteria provided, single submitter | clinical testing | |
Women's Health and Genetics/Laboratory Corporation of America, |
RCV004699433 | SCV005203106 | uncertain significance | not specified | 2024-07-09 | criteria provided, single submitter | clinical testing | Variant summary: COCH c.118G>A (p.Asp40Asn) results in a conservative amino acid change located in the LCCL domain (IPR004043) of the encoded protein sequence. Three of five in-silico tools predict a damaging effect of the variant on protein function. The variant allele was found at a frequency of 8e-05 in 251452 control chromosomes. The occurrence in several carriers suggests that this variant is likely not associated with a high penetrance, severe, early onset disease phenotype in heterozygous state. To our knowledge, no occurrence of c.118G>A in individuals affected with Hereditary hearing loss and deafness and no experimental evidence demonstrating its impact on protein function have been reported. ClinVar contains an entry for this variant (Variation ID: 1214980). Based on the evidence outlined above, the variant was classified as uncertain significance. |